小児医療を通じて未来を守る
愛媛大学小児科 ~小児医療を通じて未来を守る~

愛媛大学業績集2017

(総説)

1. 越智史博、石井榮一 (2017) JAK1/2阻害剤によるマウス血球貪食症候群モデルの治療.血液内科 74,823-829

2. 住友直方、石川広己、泉田直己、市田蕗子、岩本眞理、笠巻祐二、久賀圭祐、土井庄三郎、中西敏雄、馬場礼三、檜垣高史、堀米仁志、三谷義英、武者春樹、吉永正夫、阿部勝已、鮎沢衛、牛ノ濱大也、太田邦雄、加藤愛章、加藤太一、澤田博文、鉾碕竜範、葭葉茂樹、新博次、小川俊一、奥村謙、筒井裕之、長嶋正實、丹羽公一郎、平山篤志、堀江稔 (2017) 学校心臓検診のガイドライン.
日本循環器学会/日本小児循環器学会合同ガイドライン2016 年版 1-80

3. 越智史博 (2017)
小児急性胃腸炎・急性虫垂炎【症例から学ぶ】ノロウイルス性胃腸炎の合併
症について.小児外科

4. 福田光成 (2017) 熱性けいれんと神経炎症. 脳と発達. 診断と治療社

5. 桑原優 (2017) MMP-2. 日本小児アレルギー学会雑誌

愛媛大学小児科業績2017

1. Bergsten E, Horne AC, Arico M, Astigarraga I, Egeler MR, Filipovich AH, Ishii E, Janka GE, Ladisch S, Lehmberg K, McClain KL, Minkov M, Montgomery S, Nanduri V, Rosso DA, Henter J-I (2017)Confirmed efficacy of etoposide and dexamethasone in HLH treatment: Long term results of the cooperative HLH-2004 study.Blood 130:2728-2738.

2. Kamada M, Inui H, Kagawa T, Mineda A, Tamura T, Fujioka T, Motoki T, Hirai H, Ishii E, Minoru M (2018)What information can change the attitude of teachers toward the human papillomavirus vaccine? J Obstetr Gynecol Res 44:778-787.

3. Eguchi M, Ozaki E, Yamauchi T, Ohta M, Higaki T, Masuda K, Imoto I, Ishii E, Eguchi-Ishimae M. (2018) Manifestation of recessive combined D‐2‐, L‐2‐hydroxyglutaric aciduria in combination with 22q11.2 deletion syndrome. Am J Med Genet Part A 176:351-358.

4. Shimada H, Kiyokawa N, Miharu M, Tanizawa A, Kurosawa H, Watanabe A, Ito M, Tono C, Yuza Y, Muramatsu H, Hotta N, Okada M, Hamamoto K, Kajiwara R, Saito AM, Horibe K, Mizutani S, Adachi S, Ishii E, Shimada H (2017) Flow cytometric analysis as an additional predictive tool of treatment response in children with chronic-phase CML treated with imatinib.Pediatr Blood Cancer 64:e26478.

5. Muramatsu H, Okuno Y, Yoshida K, Shiraishi Y, Doisaki S, Narita A,Sakaguchi H, Kawashima N, Wang X, Xu Y, Chiba K, Tanaka H, Hama A, Sanada M, Takahashi Y, Kanno H, Yamaguchi H, Ohga S, Manabe A, Harigae H, Kunishima S, Ishii E, Kobayashi M, Koike K, Watanabe K, Ito E, Takata M, Yabe M, Ogawa S, Miyano M, Kojima S (2017) Clinical application of Capture-based Targeted Sequencing for Inherited Bone Marrow Failure Syndromes. Genet Med 19: 796-802.

6. Hori M, Yasumi T, Shimodera S, Shibata H, Hiejima E, Oda H, Izawa K, Kawai T, Ishimura M, Nakano N, Shirakawa R, Nishikomori R, Takada H, Morita S, Horiuchi H , Ohara O, Ishii E, Heike T (2017) A CD57+ CTL degranulation assay effectively identifies familial hemophagocytic lymphohistiocytosis type 3 patients. J Clin Immunol 37: 92-99.

7. Takashima T, Okamura M, Yeh T, Okano T, Yamashita M, Tanaka K, Hoshino A, Mitsuiki N, Takagi M, Ishii E, Imai K, Kanegane H, Morio T (2017) Multicolor flow cytometry for the diagnosis of primary immunodeficiency diseases. J Clin Immunol 37: 486-495.

8. Kodama Y, Manabe A, Kawasaki H, Kato I, Kato K, Sato A, Matsumoto K, Kato, M, Hiramatsu H, Sano H, Kaneko T, Oda M, Saito AM, Adachi S, Horibe K, Mizutani S, Ishii E, Shimada H (2017) Salvage therapy for children with relapsed or refractory Philadelphia chromosome-positive acute lymphoblastic leukemia. Pediatr Blood Cancer 64:e26423.

9. Poitras JL, Heiser D, Li L, Nguyen B, Nagai K, Duffield AS, Gamper C, Small D. (2016)Dnmt3a deletion cooperates with the Flt3/ITD mutation to drive leukemogenesis in a murine model. Oncotarget 7: 69124-69135.

10. Ichimura T, Yoshida K, Okuno Y, Yujiri T, Nagai K, Nishi M, Shiraishi Y, Ueno H, Toki T, Chiba K, Tanaka H, Muramatsu H, Hara T, Kanno H, Kojima S, Miyano S, Ito E, Ogawa S, Ohga S (2017) Diagnostic challenge of Diamond-Blackfan anemia in mothers and children by whole-exome sequencing. Int J Hematol 105: 515-520.

11. Kusakabe K, Kohno S, Inoue A, Seno T, Yonezawa S, Moritani K, Mizuno Y, Kurata M, Kitazawa R, Tauchi H, Watanabe H, Iwata S, Hirato J, Kunieda T(2018)Combined morphological, immunohistochemical and genetic analyses of medulloepithelioma in the posterior cranial fossa. Neuropathology 38:179-184.

12. Yamauchi T, Mogi M, Kan-no H, Shan B-S, Higaki A, Min L-J, Higaki T, Iwanami J, Ishii E, Horiuchi M (2018) Roles of Angiotensin II Type 2 Receptor in Mice with Fetal Growth Restriction.Hyper Res 41:157-164.

13. Bai HY, Mogi M, Nakaoka H, Kan-No H, Tsukuda K, Wang XL, Shan BS, Kukida M, Yamauchi T, Higaki A, Min LJ, Iwanami J, Horiuchi M (2017) Synergistic Inhibitory Effect of Rosuvastatin and Angiotensin II Type 2 Receptor Agonist on Vascular Remodeling. J Pharmacol Exp Ther. 358: 352-358.

14. Fukuyama N, Kurata A, Kawaguchi N, Tashiro R, Higaki T, Yokoi T, Tanabe Y, Nishiyama H, Itoh T, Kido T, Miyagawa M, Mochizuki T (2018) Two-Phase Contrast Injection Protocol for Pediatric Cardiac Computed Tomography in Children with Congenital Heart Disease. Pediatr Cardiol 39:518-525.

15. Ito M, Takahashi H, Yano H, Shimizu YI, Yano Y, Ishizaki Y, Tanaka J, Ishii E, Fukuda M (2017) High mobility group box 1 enhances hyperthermia-induced seizures and secondary epilepsy associated with prolonged hyperthermia-induced seizures in developing rats.Metab Brain Dis 32: 2095-2104.

16. Yano Y, Yano H, Takahashi H, Yoshimoto K, Tsuda S, Fujiyama K, Shimizu Y, Motoie R, Ito M, Tanaka J, Ishii E, Fukuda M (2017) Goreisan inhibits up-regulation of Aquaporin4 and formation of cerebral edema in the rat model of juvenile hypoxic-ischemic encephalopathy. Evid Based Complement Alternat Med Article ID 3209219.

17. Jogamoto T, Yamamoto Y, Fukuda M, Suzuki Y, Imai K, Takahashi Y, Inoue Y, Ohtsuka Y. (2017) Add-on stiripentol elevates serum valproate levels in patients with or without concomitant topiramate therapy. Epilepsy Res 130, 7-12.

18. Ihara K, Toda N, Fukano C, Ayabe T, Fukami M, Ogata T, Kawamura T, Urakami T, Kikuchi N, Yokota I, Takemoto K, Mukai T, Nishii A, Kikuchi T, Mori T, Shimura N, Sasaki G, Kizu R, Takubo N, Soneda S, Fujisawa T, Takaya R, Kizaki Z, Kanzaki S, Hanaki K, Matsuura N, Kasahara Y, Kosaka K, Takahashi T, Minamitani K, Matsuo S, Mochizuki H, Kobayashi K, Koike A, Horikawa R, Teno S, Tsubouchi K, Mochizuki T, Igarashi Y, Amemiya S and Sugihara S (2017) FUT2 Nonsecretor Status Links Type 1 Diabetes Susceptibility in Japanese children. Diabet Med 34: 586-589.

19. Nakano N, Mori M, Umebayashi H, Iwata N, Kobayashi N, Masunaga K, Imagawa T, Murata T, Kinjo N, Nagai K, Miyoshi M, Takei S, Yokota S, Ishii E (2017) Characterustics and outcome of intractable vasculitis syndrome in children: nationwide survey in Japan. Mod Rheumatol. 8: 1-6.

20. Kaneko N, Iwasaki T, Ito Y, Takeda H, Morikawa S, Nakano N, Kurata M, Masumoto J (2017) Applications of reconstituted inflammasomes in a cell-free system to drug discovery and elucidation of the pathogenesis of autoinflammatory disases. Inflammation and Regeneration 37;9 DOI 10.1186

21. Shinohara M, Matsumoto K (2017) Fetal Tobacco Smoke Exposure in the Third Trimester of Pregnancy Is Associated with Atopic Eczema/Dermatitis Syndrome in Infancy.Pediatr Allergy Immunol Pulmonol 30: 155-162.

22. Ishida Y, Tezuka M, Hayashi M, Inoue F (2017)Japanese childhood cancer survivors’ readiness for care as adults: a cross-sectional survey using the Transition Scales.Psychooncology 26: 1019-1026.

23. Daida A, Yoshihara H, Inai, I, Hasegawa D, Ishida Y, Urayama KY., Manabe A (2016)Risk factors for hospital-acquired Clostridium difficile infection among pediatric patients with cancer.J Pediatr Hematol Oncol 39: e167-e172.

24. Korematsu S, Fujitaka M, Ogata M, Zaitsu M, Motomura C, Kuzume K, Toku Y, Ikeda M, Odajima H (2017) Administration of the adrenaline auto-injector at the nursery/kindergarten/school in Western Japan. Asia Pac Allergy 7: 37-41.

25. Shima H, Kiyokawa N, Miharu M, Tanizawa A, Kurosawa H, Watanabe A, Ito M, Tono C, Yuza Y, Muramatsu H, Hotta N, Okada M, Hamamoto K, Kajiwara R, Saito AM, Horibe K, Mizutani S, Adachi S, Ishii E, Shimada H (2017) Flow cytometric analysis as an additional predictive tool of treatment response in children with chronic-phase CML treated with imatinib. Pediatr Blood Cancer 64:.e26478.

26. Kodama Y, Manabe A, Kawasaki H, Kato I, Kato K, Sato A, Matsumoto K, Kato, M, Hiramatsu H, Sano H, Kaneko T, Oda M, Saito AM, Adachi S, Horibe K, Mizutani S, Ishii E, Shimada H (2017) Salvage therapy for children with relapsed or refractory Philadelphia chromosome-positive acute lymphoblastic leukemia. Pediatr Blood Cancer 64: e26423.

________________________________________

(論文・英文症例報告)
1. Chijimatsu I, Imanaka Y, Tomizawa D, Eguchi M, Nishimura S, Karakawa S, Miki M, Hamamoto K, Fujita N. (2017) Azacitidine successfully maintained the second remission in an infant with KMT2A-rearranged acute lymphoblastic leukemia who relapsed after unrelated cord blood transplantation. Pediatr Blood Cancer 64:e26697.

2. Uemura S, Tamura A, Saito A, Hasegawa D, Nino N, Yokoi T, Tahara T, Kozaki A, Kishimoto K, Ishida T, Kawasaki K, Mori T, Nishimura N, Ishimae M, Eguchi M, Kosaka Y (2017) Reemergence of translocation t (11;19)(q23;p13.1) in the absence of clinically overt leukemia. Int J Hematol 106:847-851.

3. Tezuka Y, Fukuda M, Watanabe S, Nakano T, Okamoto K, Kuzume K, Yano Y, Eguchi M, Ishimae M, Ishii E, Miyazaki T (2017) Histological characterisation of visceral changes in a patient with type 2 Gaucher disease treated with enzyme replacement therapy.Blood Cells Mol Dis 68:194-199.

4. Hino K, Fukuda M, Morino T, Ogata T, Ito M, Ishii E (2017) Spinal fusion in a patient with Fukuyama congenital muscular dystrophy. Brain Dev 39:613-619.

5. Ito M, Fukuda M, Suzuki Y, Wakamoto H, Ishii E (2017) Carnitine-related hypoglycemia caused by 3 days of pivalate antibiotic therapy in a patient with severe muscular dystrophy: A case report. BMC Pediatrics 17: 73

6. Ochi F, Tauchi H, Moritani K, Yonezawa S, Miyamoto H, Suemori K, Ishii E (2017) Rothia mucilaginosa infection in a child with acute lymphoblastic leukemia: a case report. Pediatr Blood Cancer 64: 205-206

7. Ochi F, Tauchi H, Mizumoto M, Miyamoto H, Ishii E (2017) Kluyvera ascorbata infection in a neonate.Pediatr Int 59: 640-641.

8. Ochi F, Furuno K, Chong FP, Tezuka J, Mizuno Y, Aoki T, Ishii E (2017) Bilateral hydronephrosis due to obstructive ureteral stone associated with norovirus gastroenteritis. Clin Case Reports 5:936-938.

9. Kojima A, Shikata F, Okamura T, Higaki T, Ohno S, Horie M, Uchita S, Kawanishi Y, Namiguchi K, Yasugi T, Izutani H(2017 Refractory ventricular fibrillations after surgical repair of atrial septal defects in a patient with CACNA1C gene mutations – Case report. J Cardiothoracic Surg 12:118 DOI 10.1186

10. Oda F, Murakami M, Hanakawa Y, Tohyama M, Nakano N, Nishikomori R, Kambe N, Sayama K (2018) A sporadic case of granulomatous disease negative for NOD2 mutations and mimicking Blau syndrome. Clinical and Exp Derm 43:57-58.

11. Hirai H, Hamada J, Hasegawa K, Ishii E (2017) Acanthosis nigricans in a Japanese boy with hypochondroplasia due to a K650T mutation in FGFR3. Clin Pediatr Endocrinol 26:223-228.

12. Tanaka-Kubota M, Kanegane K, Morio T (2018) Hematopoietic stem cell transplantation for pulmonary alveolar proteinosis associated with primary immunodeficiency disease. Int J Hematol 5:610-614.

13. Kuwabara K, Kawarai T, Ishida Y, Miyamoto R, Oki R, Orlacchio A, Nomura Y, Fukuda M, Ishii E, Shintaku H, Kaji R (2017) A novel compound heterozygous TH mutation in a Japanese case of dopa-responsive dystonia with mild clinical course. Parkinsonism & Related Disorders 644:48-54.
________________________________________

(和文 原著・和文)
1. 西村幸士、日野ひとみ、竹本幸司、大藤佳子、楠目和代、檜垣高史、石井榮一(2018)愛媛県東予東部地区における医療圏域を越えた広域小児二次救急輪番体制の構築.日本小児科学会雑誌 122:793-799

2. 矢島知里、濱田淳平、中矢隆大、平井洋生、竹本幸司、藤澤由樹、石井榮一 (2017) 低身長精査時の軽度空腹時高血糖を契機に診断し得た MODY 2 姉妹例.愛媛医学 36: 36-40

3. 宮本真知子、手束真理、小泉宗光、山本英一、石田也寸志、石井榮一 (2017) 呼吸不全のため心肺蘇生を要したヒトメタニューモウイルス肺炎の乳児例-当院入院症例の検討.愛媛医学 36: 52-56

4. 渡邊あさみ、徳田桐子、楠目和代、福田光成、中村和幸、加藤光弘、石井榮一(2017)新たなDCX遺伝子ミスセンス変異を認めた滑脳症の男児例.愛媛医学 36: 167-170

5. 岩本麻友美、手束真理、杉田敦郎、河上早苗、宮脇零士、米澤早知子、城賀本 敏宏、桑原こずえ、小泉宗光、中野威史、山本英一、石井榮一、石田也寸志 (2017)Imatinib併用化学療法治療中に敗血症性ショックと急性呼吸窮迫症候群を合併したフィラデルフィア染色体陽性急性リンパ性白血病の1例. 日本小児血液・がん学会雑誌 54: 15-20

6. 宮本真知子、小西恭子、山本英一、中野威史、高橋由博、石田也寸志、檜垣高史、石井榮一 (2017) 肺炎+発疹のみで冠動脈瘤を来した不全型川崎病の4ヵ月男児例.Progress in Medicine 37: 805-809

7. 越智史博, 田内久道, 石井榮一 (2018)BCGワクチン接種後乳児における核酸増幅法検査のピットフォール. 小児感染免疫 29:311-315

8. 岡田恵子、森口直彦、畠山直樹、今井剛、大曽根眞也、篠田邦大、伊藤剛、田内 久道、三木瑞香、原純一、西村真一郎 (2017) 小児の好中球減少期発熱患者におけるミカファンギンの薬物動態と安全性 小児白血病研究会(JACLS)からの報告.日本小児血液・がん学会雑誌 53:117-122

9. 石田也寸志、手束真理、林三枝、井上富美子 (2017) 小児がん経験者の成人医療移行への準備状況に関する横断的実態調査. 日本小児血液・がん学会雑誌 53: 436-447

10. 桑原優、楠目和代 (2016) NA-623NRにおける呼気一酸化窒素濃度オンライン測定とオフライン測定の比較とオフライン測定の時間的安定性に関する検討. 日本小児呼吸器学会雑誌 27: 123-129

11. 山根淳文、岩本麻友美、岡本典子、渡部竜助、髙田秀実、長谷幸治、林正俊、竹本幸司、戒能幸一 (2017) 分娩外傷を伴わない下垂体茎断裂症候群による成長ホルモン分泌不全性低身長症の1例.愛媛医学36: 95-99

12. 吉田安友子、竹本幸司、勢井友香、桑原こずえ、中野威史、山本英一、石田也寸志 (2017) 中枢性思春期早発症の合併が疑われたが, mini-pubertyと診断したソトス症候群の1例.愛媛医学 36:238-243

13. 越智史博、水野由美、青木知信 (2017)血液培養陽性となった黄色ブドウ球菌感染症の臨床像. 小児感染免疫 28: 249-256.

14. 坪谷尚季、長尾みづほ、亀田桂子、鈴木尚文、桑原優、貝沼圭吾、藤澤隆夫.(2017)小麦アレルギー患児における大麦アレルギー合併を予測する因子の検討.日本小児アレルギー学会誌 31:683-691

15. 長尾みづほ、桑原優、平山淳也、貝沼圭吾、藤澤隆夫 (2017)特異的IgE抗体の多項目同時測定システムを応用した小児アレルギー疾患の感作パターン解析 マストイムノシステムズの新しい利用法. 日本小児アレルギー学会誌31: 253-261.

16. 苔口知樹、神薗淳司、志村紀彰、松島卓哉、山根浩昌、今村徳夫、石橋紳作、天本正乃、市川光太郎 (2017) 寛解導入療法中に脳性塩類喪失症候群をきたした急性リンパ性白血病の10歳男児.日本小児救急医学会雑誌16: 39-42

17. 林正俊 (2017)市立宇和島病院小児科の患者の動きからみえる地域の抱える問題.日本小児科医会報 54: 176-179

18. 林正俊 (2107)市立宇和島病院のランチョンと教育研修.南予医学雑誌18(1)

愛媛大学小児科業績 2016

【論文・英文原著】

1. Muramatsu H, Okuno Y, Yoshida K, Shiraishi Y, Doisaki S, Narita A,Sakaguchi H, Kawashima N, Wang X, Xu Y, Chiba K, Tanaka H, Hama A, Sanada M, Takahashi Y, Kanno H, Yamaguchi H, Ohga S, Manabe A, Harigae H, Kunishima S, Ishii E, Kobayashi M, Koike K, Watanabe K, Ito E, Takata M, Yabe M, Ogawa S, Miyano M, Kojima S (2016) Clinical utility of next-generation sequencing for inherited bone marrow failure syndromes.Genet Med (in press)

2. Umeda K, Adachi S, Horikoshi Y, Imai K, Terui K, Endo M, Mitsui T, Kato K, Koh K, Kajiwara R, Ito R, Otsuka Y, Inoue M, Ishii E, Yabe H (2016) Allogeneic hematopoietic stem cell transplantation for Chediak-Higashi syndrome. Pediatr Transplant 20: 271-275

3. Kurosawa H, Tanizawa A, Tono C, Watanabe A, Shima H, Ito M, Yuza Y, Hotta N, Muramatsu H, Okada M, Kajiwara R, Moriya Saito A, Mizutani S, Adachi S, Horibe K, Ishii E, Shimada H (2016) Leukostasis in children and adlescents with chronic myeloid leukemia: Japanese Pediatric Leukemia/Lymphoma Study Group. Pediatr Blood Cancer 63: 406-411

4. Hori M, Yasumi T, Shimodera S, Shibata H, Hiejima E, Oda H, Izawa K, Kawai T, Ishimura M, Nakano N, Shirakawa R, Nishikomori R, Takada H, Morita S, Horiuchi H , Ohara O, Ishii E, Heike T (2016) A CD57+ CTL degranulation assay effectively identifies familial hemophagocytic lymphohistiocytosis type 3 patients. J Clin Immunol (in press)

5. Morimoto A, Shioda Y, Imamura T, Kudo K, Kawaguchi H, Sakashita K, Yasui M, Koga Y, Kobayashi R, Ishii E, Fujimoto J, Horibe K, Bessho F, Tsunematsu Y, Imashuku S (2016) Intensified and prolonged therapy comprising cytarabine, vincristine and prednisolone improves outcome in patients with multisystem Langerhans cell histiocytosis: Results of the Japan Langerhans Cell Histiocytosis Study Group-02 Protocol Study. Int J Hematol 104: 99-109

6. Imamura T, Kiyokawa N, Kato M, Imai C, Okamoto Y, Yano M, Ohki K, Yamashita Y, Kodama Y, Saito A, Mori M, Ishimaru S, Deguchi T, Hashii Y, Shimomura Y, Hori T, Kato K, Goto H, Ogawa C, Koh K, Taki T, Manabe A, Sato A, Kikuta A, Adachi S, Horibe K, Ohara A, Watanabe A, Kawano Y, Ishii E, Shimada H (2016) Characterization of pediatric Philadelphia-negative B-cell precursor acute lymphoblastic leukemia with kinase fusions in Japan. Blood Cancer J 6: e419

7. Kodama Y, Manabe A, Kawasaki H, Kato I, Kato K, Sato A, Matsumoto K, Kato, M, Hiramatsu H, Sano H, Kaneko T, Oda M, Saito AM, Adachi S, Horibe K, Mizutani S, Ishii E, Shimada H (2016) Salvage therapy for children with relapsed or refractory Philadelphia chromosome-positive acute lymphoblastic leukemia. Pediatr Blood Cancer (in press)

8. Gao W, Higaki T, Eguchi-Ishimae M, Iwabuki H, Wu Z, Yamamoto E, Takata H, Ohta M, Imoto I, Ishii E, Eguchi M (2016) DGCR6 at proximal part of DiGeorge critical region is involved in conotruncal heart defects. Hum Genome Varia Feb 12; 2: 15004.

9. Poitras JL, Heiser D, Li L, Nguyen B, Nagai K, Duffield AS, Gamper C, Small D. (2016) Dnmt3a deletion cooperates with the Flt3/ITD mutation to drive leukemogenesis in a murine model. Oncotarget (in press)

10. Ichimura T, Yoshida K, Okuno Y, Yujiri T, Nagai K, Nishi M, Shiraishi Y, Ueno H, Toki T, Chiba K, Tanaka H, Muramatsu H, Hara T, Kanno H, Kojima S, Miyano S, Ito E, Ogawa S, Ohga S.(2016) Diagnostic challenge of Diamond-Blackfan anemia in mothers and children by whole-exome sequencing. Int J Hematol (in press)

11. Fujiwara H, Ochi T, Ochi F, Miyazaki Y, Asai H, Narita M, Okamoto S, Mineno J, Kuzushima K, Shiku H, Yasukawa M (2015) Antileukemia multifunctionality of CD4+ T cells genetically engineered by HLA class I-restricted and WT1-specific T-cell receptor gene transfer. Leukemia. 29: 2393-2401

12. Tanaka H, Fujiwara H, Ochi F, Tanimoto K, Casey N, Okamoto S, Mineno J, Kuzushima K, Shiku H, Sugiyama T, Barrett J, Yasukawa M (2016) Development of engineered T cells expressing a chimeric CD16-CD3ζ receptor to improve the clinical efficacy of mogamulizumab therapy against adult T cell leukemia. Clin Cancer Res (in press)

13. Higaki T, Chisaka T, Moritani T, Ohta M, Takata H, Yamauchi T, Ochi F, Yamaguchi Y, Konishi K, Yamamoto E, Eguchi-ishimae M, Eguchi M, Mitani Y, Ishii E (2016) Installation of multiple AED to prevent sudden death in school-aged children. Pediatr Int (in press)

14. Ishida Y, Higaki T, Hayashi M, et al (2016) Factors associated with the specific worries of childhood cancer survivors: Cross-sectional survey in Japan. Pediatr Int 58:331-7

15. Yamamoto E, Higaki T, Nakano T, Watanabe R, Konishi K, Takahashi Y, Ishida Y, Ishii E (2016) Clinical Investigation of Kawasaki Disease in Patients aged Five years or Older at Onset. Jacobs J Pediatr (in press)

16. Tomita H, Higaki T, Kobayashi T, Fujii T, Fujimoto K (2015) Stenting for curved lesions using a novel curved balloon; Preliminary experimental study. J Cardiology 66: 120-124

17. Chisaka T, Mogi M, Nakaoka H, Kan-No H, Tsukuda K, Wang XL, Bai HY, Shan BS, Kukida M, Iwanami J, Higaki T, Ishii E, Horiuchi M (2016) Low-Protein Diet-Induced Fetal Growth Restriction Leads to Exaggerated Proliferative Response to Vascular Injury in Postnatal Life. Am J Hypertens 29: 54-62

18. Kukida M, Mogi M, Ohshima K, Nakaoka H, Iwanami J, Kanno H, Tsukuda K, Chisaka T, Min LJ, Wang XL, Bai HY, Shan BS, Higaki A, Yamauchi T, Okura T, Higaki J, Horiuchi M. (2016) Angiotensin II Type 2 Receptor Inhibits Vascular Intimal Proliferation With Activation of PPARγ. Am J Hypertens. 29: 727-736

19. Mogi M, Kohara K, Nakaoka H, Kan-No H, Tsukuda K, Wang XL, Chisaka T, Bai HY, Shan BS, Kukida M, Iwanami J, Miki T, Horiuchi M. (2016) Diabetic mice exhibited a peculiar alteration in body composition with exaggerated ectopic fat deposition after muscle injury due to anomalous cell differentiation. J Cachexia Sarcopenia Muscle. 7: 213-24

20. Abe Y, Sakai T, Okumura A, Akaboshi S, Fukuda M, Haginoya K, Hamano S, Hirano K, Kikuchi K, Kubota M, Lee S, Maegaki Y, Sanefuji M, Shimozato S, Suzuki M, Suzuki Y, Takahashi M, Watanabe K, Mizuguchi M, Yamanouchi H. (2016) Manifestations and characteristics of congenital adrenal hyperplasia-associated encephalopathy. Brain Dev 38: 638-47

21. Jogamoto T, Yamamoto Y, Fukuda M, Suzuki Y, Imai K, Takahashi Y, Inoue Y, Ohtsuka Y. (2016) Add-on stiripentol elevates serum valproate levels in patients with or without concomitant topiramate therapy. Epilepsy Res (in press)

22. Hamada J, Onum H, Ochi F, Hirai H, Takemoto K, Miyoshi A, Matsushita M, Kadota Y, Ohashi J, Kawamura R, Takata Y, Nishida W, Hashida S, Ishii E, Osawa H. (2016) Endoplasmic reticulum stress induced by tunicamycin increases resistin mRNA through the PERK-ATF4-CHOP pathway in THP-1 human monocytes. J Diabetes Invest 7: 312-323

23. Ayabe T, Fukami M, Ogata T, Kawamura T, Urakami T, Kikuchi N, Yokota I, Ihara K, Takemoto K, Mukai T, Nishii A, Kikuchi T, Mori T, Shimura N, Sasaki G, Kizu R, Takubo N, Soneda S, Fujisawa T, Takaya R, Kizaki Z, Kanzaki S, Hanaki K, Matsuura N, Kasahara Y, Kosaka K, Takahashi T, Minamitani K, Matsuo S, Mochizuki H, Kobayashi K, Koike A, Horikawa R, Teno S, Tsubouchi K, Mochizuki T, Igarashi Y, Amemiya S, Sugihara S; The Japanese Study Group of Insulin Therapy for Childhood and Adolescent Diabetes (JSGIT). Variants associated with autoimmune Type 1 diabetes in Japanese children: Implications for age-specific effects of cis-regulatory haplotypes at 17q12-q21. Diabet Med (in press)

24. Ihara K, Toda N, Fukano C, Ayabe T, Fukami M, Ogata T, Kawamura T, Urakami T, Kikuchi N, Yokota I, Takemoto K, Mukai T, Nishii A, Kikuchi T, Mori T, Shimura N, Sasaki G, Kizu R, Takubo N, Soneda S, Fujisawa T, Takaya R, Kizaki Z, Kanzaki S, Hanaki K, Matsuura N, Kasahara Y, Kosaka K, Takahashi T, Minamitani K, Matsuo S, Mochizuki H, Kobayashi K, Koike A, Horikawa R, Teno S, Tsubouchi K, Mochizuki T, Igarashi Y, Amemiya S and Sugihara S; The Japanese Study Group of Insulin Therapy for Childhood and Adolescent Diabetes (JSGIT). FUT2 Nonsecretor Status Links Type 1 Diabetes Susceptibility in Japanese children. Diabet Med (in press)

25. Ishida Y, Tezuka M, Hayashi M, et al (2016) Japanese childhood cancer survivors’ readiness for care as adults: a cross-sectional survey using the Transition Scales. Psychooncology (in press)

26. Ishida Y, Qiu D, Maeda M, et al (2016) Secondary cancers after a childhood cancer diagnosis: a nationwide hospital-based retrospective cohort study in Japan. Int J Clin Oncol 21:506-16

27. Takenoshita S, Nomura K, Ohde S, Deshpande GA, Sakamoto H, Yoshida H, Urayama K, Bito S, Ishida Y, Shimbo T, Matsui K, Fukui T, Takahashi O (2016) hav ing a Mentor or a Doctoral Degree Is Helpful for Mid-Career Physicians to Publish Papers in Peer-Reviewed Journals.Tohoku J Exp Med (In press)

28. Daida A, Yoshihara H, Inai, I, Hasegawa D, Ishida Y, Urayama KY., Manabe A (2016) Risk factors for hospital-acquired Clostridium difficile infection among pediatric patients with cancer. J Pediatr Hematol Oncol (In press)

29. Mukaino A, Nakane S, Higuchi O, Nakamura H, Miyagi T, Shiroma K, Tokashiki T, Fuseya Y, Ochi K, Umeda M, Nakazato T, Akioka S, Maruoka H, Hayashi M, Igarashi S, Yokoi K, Maeda Y, Sakai W, Matsuo H, Kawakami A (2016) Insights from the ganglionic acetylcholine receptor autoantibodies in patients with Sjogren’s syndrome. Modern Rheumatol 26:708-715

愛媛大学小児科業績 2016

【論文・英文症例報告】

1.Ochi F, Tauchi H, Moritani K, Yonezawa S, Miyamoto H, Suemori K, Ishii E (2016) Rothia mucilaginosa infection in a child with acute lymphoblastic leukemia: a case report. Pediatr Blood Cancer (in press)

2.Hino H, Fukuda M, Suzuki Y, Ishii E (2016) Biphasic cuirass ventilation for treatment of an air leak
after pneumothorax in a patient with nemaline myopathy: a case report. J Anesthesia 30: 1087-1090

3.Tezuka Y, Fukuda M, Watanabe S, Nakano T, Okamoto K, Kuzume K, Yano Y, Eguchi M, Ishimae M, Ishii E, Miyazaki T (2016) Histological characterisation of visceral changes in a patient with type 2 Gaucher disease treated with enzyme replacement therapy. Blood Cells Mol Dis (in press)

4.Tezuka M, Ohta M, Ochi F, Chisaka T, Higaki T, Ishii E (2016) Successful treatment by coil embolization for infantile hemangioma with Kasabach-Meritt syndrome. Pediatric Int (in press)

5.Kojima A, Okamura T, Shikata F, Uchita S, Yamauchi T, Ohta M, Mori H, Tozawa A, Fujii S, Kawanishi Y, Higaki T, Izutani H (2016) Staged Repair of Complete Sternal Cleft and Interrupted Aortic Arch Associated With PHACES Syndrome in a Very Low Birth Weight Infant. Int Surg (in press)

6.Shikata F, Okamura T, Higaki T, Okura M, Kojima A, Uchita S, Izutani H. (2016) Aortic Coarctation 28 Days after an Arterial Switch Operation in a Neonate. Tex Heart Inst J 43: 354-356.

7.Morino T, Ogata T, Horiuchi H, Yamaoka S, Fukuda M, Miura H. (2016) Eight years of follow-up after laminectomy of calcium pyrophosphate crystal deposition in the cervical yellow ligament of patient with Coffin-Lowry syndrome: A case report. Medicine (Baltimore) 95:e4468.

8.Nagai K, Suyama Y, Koga D, Nishi M, Iida C, Tashiro K, Danjo A, Kai K, Matsuo M (2016) Anaplastic Lymphoma Kinase-Positive Anaplastic Large Cell Lymphoma with Cardiac Metastasis and Arterial Tumor Embolisms during First-Course Chemotherapy. Case Rep Oncol. 17; 9: 440-446.

9.Akaike S, Kamoi K, Tezuka M, Tomizawa D, Yoshimura R, Takagi M, Ohno-Matsui K (2016) Ocular manifestation in Myeloid/NK cell precursor acute leukemia: A case diagnosed by the flow cytometry and PCR form aqueous humor. Medline (in press)

愛媛大学小児科業績 2016

【原著・和文】

1.竹本幸司、中矢隆大、加藤文徳、牧野景、濱田淳平、戒能幸一、伊藤卓夫、藤澤由樹、石井榮一 (2016) 正期産、人工栄養児に発症したearly hypocalcemic typeのビタミンD欠乏性低カルシウム血症の1ヵ月男児例、ホルモンと臨床、特集小児内分泌学の進歩2015、62: 83-86

2.岡本健太郎、福田光成 (2016) 小児神経専門医へのインターネット上のアクセシビリテイに関する調査. 脳と発達 48: 290-291

3.越智史博,水野由美,青木知信(2017) 血液培養陽性となった黄色ブドウ球菌感染症の臨床像. 小児感染免疫.(In press)

4.元木崇裕、中川栄二、小一原玲子、高橋幸利、竹下絵里、石山昭彦、齋藤貴志、小牧宏文、須貝研司、佐々木征行(2016)免疫グロブリン治療が奏功したてんかん性脳症例. 脳と発達 2016;48:277-81.

5.石田也寸志 手束真理, 林三枝, 等 (2016) 小児がん経験者の成人医療移行への準備状況に関する横断的実態調査. 日本小児血液・がん学会雑誌 53, 2016 (印刷中)

6.歌野智之, 田中庸一, 木津純子, 神谷尚宏, 小川千登世, 石田也寸志, 細谷亮太, 真部淳 (2016)小児急性リンパ性白血病の維持療法期間におけるメルカプトプリン及びメトトレキサート投与量の推移 単施設における検討. 日本小児血液・がん学会雑誌 53:399-402

7.苔口知樹, 神薗淳司, 竹井寛和, 小林加奈, 増井美苗, 富田一郎, 石橋紳作, 天本正乃, 市川光太郎 (2016) 小児肘内障に対する超音波診断と「滑膜ひだ陥入」所見の有用性. 日本小児救急医学会雑誌 15: 14-17

8.苔口知樹, 神薗淳司, 増井美苗, 松島卓也, 山根浩昌, 石橋紳作, 今村徳夫, 天本正乃, 市川光太郎 (2016) 乳幼児発熱性疾患における体温1℃上昇あたりの心拍数と呼吸数の変化率に関する検討. 日本小児救急医学会雑誌 15: 392-396

9.苔口知樹, 志村紀彰, 神薗淳司, 村上珠菜, 山根浩昌, 今村徳夫, 石橋紳作, 天本正乃, 市川光太郎 (2016)川崎病に4回罹患後にYersinia pseudotuberculosis感染症を起こした1男児例. 小児内科 48: 116-121

10.苔口知樹, 小林加奈, 村上珠奈, 増井美苗, 富田一郎, 金奉吉, 石橋紳作, 神薗淳司, 天本正乃, 市川光太郎 (2016) 細菌性髄膜炎に4回罹患した経篩骨型頭蓋底脳瘤の男児例. 小児内科 48: 638-642

11.西村幸士 楠目和代 加賀田優紀 (2016)小児蕁麻疹患者の凝固機能についての検討 アレルギー (2016) 第65巻 2号 118-122

12.桑原優、楠目和代 (2016) NA-623N○Rにおける呼気一酸化窒素濃度オンライン測定とオフライン測定の比較とオフライン測定の時間的安定性に関する検討  日本小児呼吸器学会雑誌 第27巻 第2号 (in press)

13.長谷幸治、林正俊 (2016) シクロスポリンAが奏効している二つのWT1遺伝子変異を有するDiffuse mesangial sclerosisの一例. 日児腎誌 29:39-44

14.林正俊 (2016)市立宇和島病院小児科の患者の動きからみえる地域の抱える問題. 南予医学雑誌 17: 1-6